Gliomas, glioneuronal tumours,and neuronal tumours
完全な分子分類が実施されていないこと示すNOS（not otherwise specified）
分子学的特性は明らかにされたが，分類体系に当てはまらない腫瘍を示すNEC（not elsewhere classified）がある．
Adult-type diffuse gliomas
Astrocytoma, IDH-mutant
Astrocytoma, IDH-mutant, grade 2
Astrocytoma, IDH-mutant, grade 3
Astrocytoma, IDH-mutant, grade 4
Oligodendroglioma, IDH-mutant and 1p/19q-codeleted
Oligodendroglioma, IDH-mutant and 1p/19q-codeleted, grade 2
Oligodendroglioma, IDH-mutant and 1p/19q-codeleted, grade 3
Glioblastoma, IDH-wildtype
Paediatric-type diffuse low-grade gliomas
Diffuse astrocytoma, MYB- or MYBL1-altered
Angiocentric glioma
Polymorphous low-grade neuroepithelial tumour of the young
Diffuse low-grade glioma, MAPK pathway-altered
Paediatric-type diffuse high-grade gliomas
Diffuse midline glioma, H3 K27-altered
Diffuse hemispheric glioma, H3 G34-mutant
Diffuse paediatric-type high-grade glioma, H3-wildtype and IDH-wildtype
Infant-type hemispheric glioma
Circumscribed astrocytic gliomas
Pilocytic astrocytoma
High-grade astrocytoma with piloid features
Pleomorphic xanthoastrocytoma
Subependymal giant cell astrocytoma
Chordoid glioma
Astroblastoma, MN1-altered
Glioneuronal and neuronal tumours
Ganglioglioma
Gangliocytoma
Desmoplastic infantile ganglioglioma
Desmoplastic infantile astrocytoma
Dysembryoplastic neuroepithelial tumour
Diffuse glioneuronal tumour with oligodendroglioma-like features and nuclear clusters (provisional entity)
Papillary glioneuronal tumour
Rosette-forming glioneuronal tumour
Myxoid glioneuronal tumour
Diffuse leptomeningeal glioneuronal tumour
Multinodular and vacuolating neuronal tumour
Dysplastic cerebellar gangliocytoma(Lhermitte-Duclos disease)
Central neurocytoma
Extraventricular neurocytoma
Cerebellar liponeurocytoma
Ependymal tumours
Supratentorial ependymoma, NOS
Supratentorial ependymoma, ZFTA fusion-positive
Supratentorial ependymoma, YAPI fusion-positive
Posterior fossa ependymoma, NOS
Posterior fossa group A (PFA) ependymoma
Posterior fossa group B (PFB) ependymoma
Spinal ependymoma, NOS
Spinal ependymoma, MYCN-amplified
Myxopapillary ependymoma
Subependymoma
Choroid plexus tumours
Choroid plexus papilloma
Atypical choroid plexus papilloma
Choroid plexus carcinoma
Embryonal tumours
Medulloblastomas, molecularly defined
Medulloblastoma, WNT-activated
Medulloblastoma, SHH-activated and TP53-wildtype
Medulloblastoma, SHH-activated and TP53-mutant
Medulloblastoma, non-WNT/non-SHH
Medulloblastomas, histologically defined
Medulloblastoma, histologically defined
Desmoplastic nodular medulloblastoma
Medulloblastoma with extensive nodularity
Large cell medulloblastoma
anaplastic medulloblastoma
Other CNS embryonal tumours Introduction
Atypical teratoid/rhabdoid tumour
Cribriform neuroepithelial tumour(provisional entity)
Embryonal tumour with multilayered rosettes
CNS neuroblastoma, FOXR2-activated
CNS tumour with BCOR internal tandem duplication
CNS embryonal tumour, NEC/NOS
Pineal tumours
Pineocytoma
Pineal parenchymal tumour of intermediate differentiation
Pineoblastoma
Papillary tumour of the pineal region
Desmoplastic myxoid tumour of the pineal region, SMARCB1-mutant(provisional entity)
Cranial and paraspinal nerve tumours
Schwannoma
Neurofibroma
Plexiform neuroblastoma
Perineurioma
Hybrid nerve sheath tumours
Malignant melanotic nerve sheath tumour
Malignant peripheral nerve sheath tumour
Cauda equina neuroendocrine tumour(previously paraganglioma)
Meningioma
Meningioma
Mesenchymal, non-meningothelial tumours involving the CNS
Fibroblastic and myofibroblastic tumours
Solitary fibrous tumour
Vascular tumours
Cavernous haemangioma
Capillary haemangioma
Arteriovenous malformation
Haemangioblastoma
Skeletal muscle tumours
Embryonal rhabdomyosarcoma
Alveolar rhabdomyosarcoma
Rhabdomyosarcoma, pleomorphic-type
Spindle cell rhabdomyosarcoma
Tumours of uncertain differentiation
Intracranial mesenchymal tumour,FET::CREB fusion-positive(provisional entity)
CIC-rearranged sarcoma
Primary intracranial sarcoma,DICER1-mutant
Ewing sarcoma
Chondrogenic tumours
Mesenchymal chondrosarcoma
Chondrosarcoma
Dedifferentiated chondrosarcoma
Notochordal tumours
Chordoma
Melanocytic tumours
Diffuse meningeal melanocytic neoplasms
Meningeal melanocytosis
Meningeal melanomatosis
Circumscribed meningeal melanocytic neoplasms
Meningeal melanocytoma
Meningeal melanoma
Haematolymphoid tumours involving the CNS
CNS lymphomas
Primary diffuse large B-cell lymphoma of the CNS
Lymphomatoid granulomatosis
Lymphomatoid granulomatosis, grade1
Lymphomatoid granulomatosis, grade2
Lymphomatoid granulomatosis, grade3
Intravascular large B-cell lymphoma
Miscellaneous rare lymphomas in the CNS
MALT lymphoma of the dura
Lymphoplasmatic lymphoma
Follicular lymphoma
Anaplastic large cell lymphoma(ALK+/ALK-)
T-cell lymphoma
NK/T-cell lymphomas
Histiocytic tumours
Erdheim-Chester disease
Rosai-Dorfman disease
Juvenile xanthogranuloma
Langerhans cell histiocytosis
Histiocytic sarcoma
Germ cell tumours
Mature teratoma
Immature teratoma
Teratoma with somatic-type malignancy
Germinoma
Embryonal carcinoma
Yolk sac tumor
Choriocarcinoma
Mixed germ cell tumour
Tumours of the sellar region
Adamantinomatous craniopharyngioma
Papillary craniopharyngioma
Pituicytoma
Granular cell tumour of the sellar region
Spindle cell oncocytoma
Pituitary adenoma / pituitary neuroendocrine tumour(PitNET)
Pituitary blastoma
完全な分子分類が実施されていないこと示すNOS（not otherwise specified）
分子学的特性は明らかにされたが，分類体系に当てはまらない腫瘍を示すNEC（not elsewhere classified）がある．
Adult-type diffuse gliomas
Astrocytoma, IDH-mutant
Astrocytoma, IDH-mutant, grade 2
Astrocytoma, IDH-mutant, grade 3
Astrocytoma, IDH-mutant, grade 4
Oligodendroglioma, IDH-mutant and 1p/19q-codeleted
Oligodendroglioma, IDH-mutant and 1p/19q-codeleted, grade 2
Oligodendroglioma, IDH-mutant and 1p/19q-codeleted, grade 3
Glioblastoma, IDH-wildtype
Paediatric-type diffuse low-grade gliomas
Diffuse astrocytoma, MYB- or MYBL1-altered
Angiocentric glioma
Polymorphous low-grade neuroepithelial tumour of the young
Diffuse low-grade glioma, MAPK pathway-altered
Paediatric-type diffuse high-grade gliomas
Diffuse midline glioma, H3 K27-altered
Diffuse hemispheric glioma, H3 G34-mutant
Diffuse paediatric-type high-grade glioma, H3-wildtype and IDH-wildtype
Infant-type hemispheric glioma
Circumscribed astrocytic gliomas
Pilocytic astrocytoma
High-grade astrocytoma with piloid features
Pleomorphic xanthoastrocytoma
Subependymal giant cell astrocytoma
Chordoid glioma
Astroblastoma, MN1-altered
Glioneuronal and neuronal tumours
Ganglioglioma
Gangliocytoma
Desmoplastic infantile ganglioglioma
Desmoplastic infantile astrocytoma
Dysembryoplastic neuroepithelial tumour
Diffuse glioneuronal tumour with oligodendroglioma-like features and nuclear clusters (provisional entity)
Papillary glioneuronal tumour
Rosette-forming glioneuronal tumour
Myxoid glioneuronal tumour
Diffuse leptomeningeal glioneuronal tumour
Multinodular and vacuolating neuronal tumour
Dysplastic cerebellar gangliocytoma(Lhermitte-Duclos disease)
Central neurocytoma
Extraventricular neurocytoma
Cerebellar liponeurocytoma
Ependymal tumours
Supratentorial ependymoma, NOS
Supratentorial ependymoma, ZFTA fusion-positive
Supratentorial ependymoma, YAPI fusion-positive
Posterior fossa ependymoma, NOS
Posterior fossa group A (PFA) ependymoma
Posterior fossa group B (PFB) ependymoma
Spinal ependymoma, NOS
Spinal ependymoma, MYCN-amplified
Myxopapillary ependymoma
Subependymoma
Choroid plexus tumours
Choroid plexus papilloma
Atypical choroid plexus papilloma
Choroid plexus carcinoma
Embryonal tumours
Medulloblastomas, molecularly defined
Medulloblastoma, WNT-activated
Medulloblastoma, SHH-activated and TP53-wildtype
Medulloblastoma, SHH-activated and TP53-mutant
Medulloblastoma, non-WNT/non-SHH
Medulloblastomas, histologically defined
Medulloblastoma, histologically defined
Desmoplastic nodular medulloblastoma
Medulloblastoma with extensive nodularity
Large cell medulloblastoma
anaplastic medulloblastoma
Other CNS embryonal tumours Introduction
Atypical teratoid/rhabdoid tumour
Cribriform neuroepithelial tumour(provisional entity)
Embryonal tumour with multilayered rosettes
CNS neuroblastoma, FOXR2-activated
CNS tumour with BCOR internal tandem duplication
CNS embryonal tumour, NEC/NOS
Pineal tumours
Pineocytoma
Pineal parenchymal tumour of intermediate differentiation
Pineoblastoma
Papillary tumour of the pineal region
Desmoplastic myxoid tumour of the pineal region, SMARCB1-mutant(provisional entity)
Cranial and paraspinal nerve tumours
Schwannoma
Neurofibroma
Plexiform neuroblastoma
Perineurioma
Hybrid nerve sheath tumours
Malignant melanotic nerve sheath tumour
Malignant peripheral nerve sheath tumour
Cauda equina neuroendocrine tumour(previously paraganglioma)
Meningioma
Meningioma
Mesenchymal, non-meningothelial tumours involving the CNS
Fibroblastic and myofibroblastic tumours
Solitary fibrous tumour
Vascular tumours
Cavernous haemangioma
Capillary haemangioma
Arteriovenous malformation
Haemangioblastoma
Skeletal muscle tumours
Embryonal rhabdomyosarcoma
Alveolar rhabdomyosarcoma
Rhabdomyosarcoma, pleomorphic-type
Spindle cell rhabdomyosarcoma
Tumours of uncertain differentiation
Intracranial mesenchymal tumour,FET::CREB fusion-positive(provisional entity)
CIC-rearranged sarcoma
Primary intracranial sarcoma,DICER1-mutant
Ewing sarcoma
Chondrogenic tumours
Mesenchymal chondrosarcoma
Chondrosarcoma
Dedifferentiated chondrosarcoma
Notochordal tumours
Chordoma
Melanocytic tumours
Diffuse meningeal melanocytic neoplasms
Meningeal melanocytosis
Meningeal melanomatosis
Circumscribed meningeal melanocytic neoplasms
Meningeal melanocytoma
Meningeal melanoma
Haematolymphoid tumours involving the CNS
CNS lymphomas
Primary diffuse large B-cell lymphoma of the CNS
Lymphomatoid granulomatosis
Lymphomatoid granulomatosis, grade1
Lymphomatoid granulomatosis, grade2
Lymphomatoid granulomatosis, grade3
Intravascular large B-cell lymphoma
Miscellaneous rare lymphomas in the CNS
MALT lymphoma of the dura
Lymphoplasmatic lymphoma
Follicular lymphoma
Anaplastic large cell lymphoma(ALK+/ALK-)
T-cell lymphoma
NK/T-cell lymphomas
Histiocytic tumours
Erdheim-Chester disease
Rosai-Dorfman disease
Juvenile xanthogranuloma
Langerhans cell histiocytosis
Histiocytic sarcoma
Germ cell tumours
Mature teratoma
Immature teratoma
Teratoma with somatic-type malignancy
Germinoma
Embryonal carcinoma
Yolk sac tumor
Choriocarcinoma
Mixed germ cell tumour
Tumours of the sellar region
Adamantinomatous craniopharyngioma
Papillary craniopharyngioma
Pituicytoma
Granular cell tumour of the sellar region
Spindle cell oncocytoma
Pituitary adenoma / pituitary neuroendocrine tumour(PitNET)
Pituitary blastoma
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